A rare case of cervical Rhabdomyosarcoma in an Adolescent- A case report
DOI:
https://doi.org/10.17576/JSA.2024.1402.04Keywords:
Cervical Embryonal Rhabdomyosarcoma, ERMS, adolescent polyp, Paediatrics and adolescent gynecology, PAG, Fertility sparing surgery, case reportAbstract
We present a rare case of cervical embryonic rhabdomyosarcoma (ERMS) in adolescents, managed with fertility-sparing surgery and chemotherapy. This type of malignant tumour is rare, and the management is not codified. A 15-year-old girl presented with a tongue-like mass per vagina and abnormal discharge. She underwent vaginoscopy under anaesthesia, which revealed a polyp from the endocervix. Hysteroscopic resection was performed, and histopathology showed ERMS. Postoperative imaging suggests the presence of residual local disease without evidence of distant metastasis. A multidisciplinary team (MDT) meeting was conducted, and the family opted for fertility-sparing management. The patient underwent repeat hysteroscopy-guided local excision, followed by eight cycles of chemotherapy, with close surveillance. In conclusion, polyps are rather odd in adolescents; malignancy should always be suspected. Fertility-sparing surgery with chemotherapy is a plausible option in well-selected cases.References
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